Although the disease has been described for over a century. Pdf henochschonlein purpura hsp is the most common vasculitis in children. Henochschonlein purpura anaphylactoid purpura, vascular purpura internal medicine an acquired form of small vessel vasculitis with igadominant immune deposits affecting small vesselsarteries, capillaries, venules, typically of the skin, gut, and glomeruli, associated with arthralgia andor arthritis. It is characterized by palpable purpura andor joint, abdominal or renal. Please use one of the following formats to cite this article in your essay, paper or report. There are many different conditions that feature vasculitis. A case of hsp is reported in a 36yearold female with. Henochschonlein purpura hsp is a rare disease that causes the blood vessels in your skin to become irritated and swollen.
Henoch schonlein purpura was confirmed by finding iga deposition on vessels within gastric and duodenal mucosa, while immunohistochemistry also identified dense focal t cell infiltration in. Each of the forms of vasculitis tends to involve certain. Hsp can affect blood vessels in the bowel and the kidneys, as well. Purpura occur in all cases, joint pains and arthritis in 80%, and abdominal pain in 62%. Hypersensitivity vasculitis and henoch schonlein purpura.
It affects children, mainly males, in 90% of cases the four main clinical features include purpura rash, abdominal pain, arthralgia and renal involvement. Henoch schonlein purpura causes skin rash, pain in the abdomen, and joint inflammation. Henochschonlein purpura hsp is vasculitis of the small vessels, the most common vasculitis of the childhood and is uncommon in adults. Henochschonlein purpura hsp is an immune mechanism leukocytoclastic vasculitis with small vessel involvement. Henochschonlein purpura symptoms and causes mayo clinic. It affects children, mainly males, in 90% of cases the four main clinical features include purpura. Henoch schonlein purpura also known as iga vasculitis is a disorder that causes the small blood vessels in your skin, joints, intestines, and kidneys to become inflamed and bleed.
Henochschonlein purpura hsp is the most common small vessel leukocytoclastic vasculitis during childhood. Henoch schonlein purpura hsp, also called immunoglobulin a vasculitis igav, is a vascular disease that primarily affects small blood vessels. Hsp is most common in younger pts clinical red maculopapules on legs and buttocks. When the blood vessels bleed, you get a rash called purpura. Henochschonlein purpura definition of henochschonlein.
Hsp is usually selflimiting in 94% of children and 89% of adults. Cursaba con evolucion torpida y complicaciones gastrointestinales y renales. Pdf hemorragia pulmonar, una complicacion poco frecuente en. The role of corticosteroid in hemorrhagic bullous henoch schonlein purpura. Henochschonlein purpura hsp is a form of blood vessel inflammation or vasculitis. Gastroenterology research practice 2010, article id 597648. Some include gastrointestinal hemorrhage as a fourth criterion. The treatment of henoch schonlein purpura is directed toward the most significant area of involvement.
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